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EN_B00000_S05963_W000009 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000010 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000011 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000012 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000013 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000014 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000027 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000028 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000029 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Jerusalem is actually 100 per 100,000. So, uh, quite a significant difference. The incidence obviously then varies by region. Most cases are diagnosed in middle age.",
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EN_B00000_S05963_W000030 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And the skin. And typically when you see this, it's going to start in the mouth and then it will start to occur elsewhere on the body.",
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EN_B00000_S05963_W000031 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " It's typically widespread at the later stages and more progressed stages of the disease. The palms and soles are usually spared, and that's an important distinction from the n... | EN_B00000_S05963_W000031.mp3 | [
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EN_B00000_S05963_W000032 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000033 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000034 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Gross appearance, you have painful flaccid blisters of the mucous membrane and skin. Usually they're eroded. The erosions can coincide with the blisters. If you do see the bli... | EN_B00000_S05963_W000034.mp3 | [
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EN_B00000_S05963_W000035 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000036 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Notice that this is eroded, so you don't see the blister and it's very easy for these blisters to erode because there's a lot of friction in the mouth and, uh, you know, the t... | EN_B00000_S05963_W000036.mp3 | [
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EN_B00000_S05963_W000037 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000038 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And you can see here that it can spread, uh, to the trunk. So, uh, again, you don't really see any, uh, current blisters. Uhm, but you'll wanna look for one because that's wher... | EN_B00000_S05963_W000038.mp3 | [
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EN_B00000_S05963_W000039 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " So here you do actually see some blisters. And notice that, uh, that you have different stages of healing. So you've got some eroded blisters. You've got active blisters. Uh, so... | EN_B00000_S05963_W000039.mp3 | [
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EN_B00000_S05963_W000040 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Or at least, uh, what you see underneath the blister is, uh, red tissue.",
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EN_B00000_S05963_W000041 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " The microscopic findings, you'll see a super basal or cleft.",
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EN_B00000_S05963_W000042 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " I'm gonna show you a picture of that of course. Uh, you may also see dermal inflammatory cell infiltrate with eosinophils. Remember those are those pink, uh, white blood cells... | EN_B00000_S05963_W000042.mp3 | [
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EN_B00000_S05963_W000043 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Direct immunofluorescence is really important to understand because the USMLE likes to show you this one. Uh, they'll show you a picture of this and they'll ask you in the ans... | EN_B00000_S05963_W000043.mp3 | [
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EN_B00000_S05963_W000044 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " You'll see IgG and C3 deposits in the pattern of a broad linear net-like band. And of course it's going to be in the epidermal layer because this targets desmosomes of the ker... | EN_B00000_S05963_W000044.mp3 | [
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EN_B00000_S05963_W000045 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000046 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Uh, and, uh, notice that you have here your blister cavity. Uh, notice that the basement membrane is intact. That's this sort of fuchsia-like line underneath these basal cells... | EN_B00000_S05963_W000046.mp3 | [
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EN_B00000_S05963_W000047 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000048 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000049 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Uh, you have what are called here, uh, acanthocytes, that's just cells that have, uh, cleaved away from each other, keratinocytes have cleaved away from each other, uh, due to... | EN_B00000_S05963_W000049.mp3 | [
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EN_B00000_S05963_W000050 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " This is that tomb stoning again. All the tomb stoning is, what it means is that you see basal cells detached from the rest of the epidermis. So they look like tombs, because r... | EN_B00000_S05963_W000050.mp3 | [
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EN_B00000_S05963_W000051 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Again, notice the basement membrane is intact. That's this kind of pinkish fuchsia layer underneath the stratum base alley.",
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EN_B00000_S05963_W000052 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " This is immunofluorescence. So, uh, immunofluorescence, if it stains positive, it's going to be a lighter neon green color, whereas the negative area is going to be a darker g... | EN_B00000_S05963_W000052.mp3 | [
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EN_B00000_S05963_W000053 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000054 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Again here, you can appreciate that fish net-like pattern and a very broad, uh, band.",
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} | EN_B00000_S05963_W000054.mp3 | [
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EN_B00000_S05963_W000055 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " The diagnosis is by biopsy, which you can look just with H and E stain as we saw, or you can do immunofluorescence, or you can do both, it's usually done with both. Remember y... | EN_B00000_S05963_W000055.mp3 | [
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EN_B00000_S05963_W000056 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " The differential diagnosis is Bullis-Pemphigoid. Bullis-Pemphigoid, as we're gonna see, is Nikolsky negative. The blisters are often stronger, so you're more likely to see more... | EN_B00000_S05963_W000056.mp3 | [
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EN_B00000_S05963_W000057 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " With bolus pemphigoid, they tend to be pruritic, whereas with pemphigus vulgaris, they tend to be really painful. Uh, with bolus pemphigoid, you're less likely to see ulcers o... | EN_B00000_S05963_W000057.mp3 | [
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EN_B00000_S05963_W000058 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000059 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000060 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Atheistomatitis is just a canker sore. These are confined to the oral region. They're painful, but they're self-limited, so they're very isolated, uh, lesions.",
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EN_B00000_S05963_W000061 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000062 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000063 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Uh, so immunomodulators would be things like mycophenolate. However, I've read that rituximab can be used as well. Topical lidocaine can be given for pain.",
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EN_B00000_S05963_W000064 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " It's also characterized by IgG autoantibodies. However, these autoantibodies target the hemidesmosomes. Remember, the hemidesmosomes are what attach the stratum basale cells t... | EN_B00000_S05963_W000065.mp3 | [
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EN_B00000_S05963_W000066 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000068 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000069 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000070 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And the blisters may be filled with serous fluid or later blood and that's why when you look at these blisters some of them look yellow and some of them look red.",
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EN_B00000_S05963_W000071 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000072 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000073 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000074 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000075 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And the blister cavity in dermis can also be infiltrated here with ESNFLs.",
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EN_B00000_S05963_W000076 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " With direct immunofluorescence, it will also reveal IgG and C3 deposits.",
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EN_B00000_S05963_W000077 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000078 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Here you can see eosinophils. This is, you're just looking at dermis here. Uh, you see some, uh, some edema with some space in between, uh, the, the fibers. Uhm, notice also, ... | EN_B00000_S05963_W000078.mp3 | [
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EN_B00000_S05963_W000079 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000080 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " So right here, this is a good example, you see some periartil or infiltrate. Uhm, you see infiltration elsewhere in the dermis but you notice again the separation is at the le... | EN_B00000_S05963_W000080.mp3 | [
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EN_B00000_S05963_W000081 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"speaker": "EN_B00000_S05963",
"text": " Again here you can see some eosinophils, uh, infiltrating, uh, in, in this case into the, uh, the blister cavity.",
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EN_B00000_S05963_W000082 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"speaker": "EN_B00000_S05963",
"text": " Here's immunofluorescence. So notice how it's different here. You just see a very thin line. The epidermis is intact.",
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EN_B00000_S05963_W000083 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"speaker": "EN_B00000_S05963",
"text": " You don't see any of that fishnetting. So here's Pemphigus vulgaris. You see fishnetting here because the, the antibodies are in and around the keratinocytes. Uh, whereas here,... | EN_B00000_S05963_W000083.mp3 | [
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EN_B00000_S05963_W000084 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " The diagnosis for Bull's Pemphigoid is the exact same way we go about diagnosing Pemphigus vulgaris and that's a biopsy of a fresh lesion. It's not going to help you if you do... | EN_B00000_S05963_W000084.mp3 | [
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EN_B00000_S05963_W000085 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And the treatment is pretty much the same as pemphigus vulgaris as well. The mainstay of treatment is corticosteroids, immunomodulators can be used for steroid sparing, and an... | EN_B00000_S05963_W000085.mp3 | [
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EN_B00000_S05963_W000086 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"speaker": "EN_B00000_S05963",
"text": " Traumatic blisters, we're not going to spend too much time on. They're pretty fairly easy to diagnose. Uhm, these are just isolated blisters that may occur from a variety of f... | EN_B00000_S05963_W000086.mp3 | [
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EN_B00000_S05963_W000087 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Uh, differentiating traumatic blisters from blistering disorders is based on clinical history. Uh, pretty easy. I mean, they're in isolation, or a patient may say, I was walki... | EN_B00000_S05963_W000087.mp3 | [
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EN_B00000_S05963_W000088 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " I was trying to climb up Machu Picchu, the mountain where Machu Picchu is and I was using a walking stick and I blistered my finger.",
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EN_B00000_S05963_W000089 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " Uh, from, uh, well, more of a hiking stick, I guess. Uh, but I was holding onto it so tightly that I blistered my finger. I have pretty nasty blood blister. So these can happe... | EN_B00000_S05963_W000089.mp3 | [
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EN_B00000_S05963_W000091 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000093 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000094 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000095 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05963_W000096 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05973_W000000 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05973_W000001 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05973_W000002 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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EN_B00000_S05973_W000003 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " If they don't rock out with your food, that's pretty fucking annoying. The grounds for anger.",
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EN_B00000_S05973_W000004 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " We had a situation here, it was a late night Friday, ordered pizzas, the guy came and I looked, he had a backpack.",
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EN_B00000_S05973_W000005 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"id": "EN_B00000_S05973_W000005",
"language": "en",
"speaker": "EN_B00000_S05973",
"text": " Which does not fit a pizza in it unless it's on its side and he takes it out and he looks so frazzled, frazzled, frazzled, frazzled. If only he was frazzled.",
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EN_B00000_S05973_W000006 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " And I just said, don't worry about it, man. It's all good. Like I was like, this poor bastard.",
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EN_B00000_S05973_W000007 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " The definition of a Gronk, and we just used real life examples, is someone who complains or tries to get a refund on food where they know in their heart of hearts they wouldn'... | EN_B00000_S05973_W000007.mp3 | [
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EN_B00000_S05973_W000008 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"speaker": "EN_B00000_S05973",
"text": " It's a massive cronk move. If you're taking advantage of this platform, like you're going, ah, they're big, they don't worry. It's not, not an issue for them. Like that's a ma... | EN_B00000_S05973_W000008.mp3 | [
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EN_B00000_S05973_W000009 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " I mean, you get cold food all the time. You ex- like think about what you're, you're expecting. You're expecting a super hot pizza that's been delivered on a bike. Like that f... | EN_B00000_S05973_W000009.mp3 | [
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EN_B00000_S05973_W000010 | hf://datasets/amphion/Emilia-Dataset@bcaad00d13e7c101485990a46e88f5884ffed3fc/EN/EN-B000003.tar | {
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"text": " You get it hot from the restaurant. It could get cold when you take it home. And so if you then complain about a cold pizza, because the delivery guys brought it to you, the dif... | EN_B00000_S05973_W000010.mp3 | [
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